Abdominal Wall Conditions
Overview of Anterior Abdominal Wall Defects
- Frequent neonatal surgical condition involving failure of midgut return during embryonic development (11th week gestation).
- Leads to abdominal contents protruding through the abdominal wall defect.
Omphalocele
- Central abdominal wall defect > 4 cm with a membranous sac (outer layer: amnion, inner layer: peritoneum).
- Smaller defects (< 4 cm): Referred to as umbilical cord hernias.
- Associated anomalies (βΌ50%):
- Beckwith-Wiedemann syndrome:
- Gigantism, macroglossia, and umbilical defect.
- Chromosomal abnormalities: Trisomies 13, 15, 18, 21.
- Bladder or cloacal exstrophy, Pentalogy of Cantrell (omphalocele, anterior diaphragmatic hernia, sternal cleft, ectopia cordis, intracardiac defect).
- Beckwith-Wiedemann syndrome:
- Initial Management:
- Preserve the intact omphalocele sac.
- Prevent hypothermia.
- Comprehensive diagnostic workup to identify associated anomalies.
- Surgical Management:
- Primary closure for small to medium defects.
- Large defects: Closed with prosthetic patch (e.g., Gore-Tex), Surgisis, skin flap, or silo for staged reduction.
- Giant omphaloceles: Treated with escharotic agents (e.g., povidone-iodine, silver nitrate) to thicken and epithelialize the sac.
- Prognosis:
- Dependent on lung maturity and the severity of associated anomalies.
Gastroschisis
- Defect located to the right of an intact umbilical cord, typically 4 cm in diameter, with no sac covering the abdominal viscera.
- Direct exposure to amniotic fluid causes intestinal thickening, edema, and inflammation.
- Associated findings:
- Intestinal atresia: Present in 15% of cases.
- Other major anomalies are rare.
- Initial Management:
- Infants placed in a warm, saline-filled plastic bowel bag up to the nipple line to minimize heat and fluid loss.
- Allows for inspection of the bowel to avoid twisting.
- Surgical Management:
- Primary reduction of eviscerated contents is successful in 50%-80% of cases.
- If unsuccessful, a ringed silo bag is used for gradual reduction over several days, followed by operative closure.
- Sutureless closure with a watertight clear dressing may also be performed.
- Intra-abdominal pressure should be < 15 mm Hg to avoid compartment syndrome.
- Delayed closure performed in cases of associated intestinal atresia or stenosis.
- For larger defects, a prosthetic patch (Gore-Tex) is placed, followed by skin closure.
- Complications:
- Necrotizing enterocolitis (NEC): Reported in 20% of patients after gastroschisis repair.
- Undescended testis: Found in 10%-20% of infants.
- Testes are repositioned into the abdominal cavity without orchidopexy at the time of repair.
- Orchidopexy performed later if necessary.
- Prolonged ileus and risk of short gut syndrome.
- Cholestasis due to prolonged total parenteral nutrition (TPN) support.
Hernias in Pediatric Surgery
Inguinal Hernia
- Incidence:
- Term infants: 3%-5%.
- Premature infants: 9%-11%.
- Affects boys six times more often than girls.
- 60% on the right side, 30% on the left side, 10% bilateral.
- Most are indirect and congenital in nature.
Pathophysiology
- Caused by the persistence of the processus vaginalis, which normally obliterates by the ninth month of gestation or shortly after birth.
- Can present as:
- Scrotal hernia with protrusion of intestine, ovaries, omentum, or communicating hydrocele.
Diagnosis
- Based on clinical history and physical examination.
- Transillumination may not be reliable, as thin-walled bowel loops can transilluminate.
- Silk glove sign: A diagnostic clue felt by palpation of the cord.
- Ultrasound may be helpful if there is suspicion of associated conditions like epididymitis or testicular torsion.
Risks
- Major risks include bowel incarceration and strangulation.
- Premature infants have a higher risk of incarceration in the first year of life.
Timing of Surgery
- Historically performed before hospital discharge in premature infants.
- Current concerns involve the risk of neurodevelopmental delay with general anesthesia, favoring delayed repair.
- Elective repair may be deferred until 1 year of age to reduce postoperative apnea risk.
- Incarcerated hernia:
- Reduction should be attempted first.
- Surgery performed 24-48 hours later once tissue edema subsides.
- Non-reducible incarcerated hernia is a surgical emergency.
Contralateral Exploration
- Routine exploration for contralateral patent processus vaginalis is common due to its incidence (4%-65%).
- The decision to explore the asymptomatic contralateral side in toddlers is still debated.
- Many surgeons opt for contralateral exploration in children 2 years or younger.
Laparoscopic vs. Open Repair
- Laparoscopic repair is increasingly used.
- A meta-analysis comparing laparoscopic vs open repair showed no definite advantage for either technique.
Umbilical Hernia
- Tends to close spontaneously in about 80% of cases.
- Elective repair is generally deferred until the child is around 5 years of age.
- Incarceration of umbilical hernias is extremely rare.
When to Consider Early Repair
- If the hernia enlarges over time.
- If the fascial defect is larger than 2 cm.
- Large skin proboscis (>3 cm) may develop if left untreated, leading to poor postoperative cosmesis.
Surgical Approach
- Primary repair is always performed.
- Prosthetic patch should never be considered.
Key Terms Highlighted:
- Inguinal hernia
- Processus vaginalis
- Bowel incarceration
- Strangulation
- Contralateral exploration
- Laparoscopic repair
- Umbilical hernia
- Primary repair
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