Aneurysm of the Abdominal Aorta (AAA)
Basics
- Two types:
- True aneurysm: involves all three vessel wall layers.
- False (pseudoaneurysm): intimal and medial layers disrupted; dilated segment held by adventitia only; higher rupture risk.
- AAA is the most common true arterial aneurysm, usually infrarenal.
- Aortic diameter β₯3 cm is aneurysmal.
- Men: diameter predictive of clinical events; women: aortic scaling index (diameter/BSA) more predictive.
Epidemiology
- Prevalence: 2-8% in developed countries; 4-8% occult AAA in older men on ultrasound.
- 90% of AAA >4 cm related to atherosclerosis.
- Male predominance.
- Incidence: 15,000 deaths/year in US; 0.4-0.67% in Western populations.
- Incidence increases with age; men 65-74: 55/100,000 patient-years, men >85: 298/100,000.
- Mortality decreased by 50% since 1990s due to smoking decline, screening, early intervention.
Etiology and Pathophysiology
- Degradation of elastin and collagen in aortic wall causes aneurysm formation.
- Causes: inflammation, degenerative disorders, vasculitis, infection, trauma; majority due to atherosclerosis.
- Natural course: progressive expansion; smoking accelerates growth.
Genetics
- Familial AAAs: polygenic inheritance.
- Monogenic syndromes (Marfan, Ehlers-Danlos, Loeys-Dietz) mainly cause thoracoabdominal aneurysms.
Risk Factors
- Older age, male, Caucasian, family history, smoking, hypertension, hyperlipidemia, atherosclerosis, peripheral aneurysms, obesity.
Prevention
- Address cardiovascular risk factors aggressively.
- Screening recommended for men 65-75 years with smoking history.
Associated Conditions
- Hypertension, myocardial infarction, heart failure, carotid atherosclerosis, peripheral arterial disease, tobacco abuse.
- 20% AAA patients have concurrent thoracic aneurysm.
Diagnosis
- Asymptomatic AAAs often found on screening.
- USPSTF: one-time ultrasound screen for men 65-75 years with smoking history; selective screening for nonsmoking men 65-75 with risk factors; women with first-degree relative with AAA also considered.
- Symptomatic triad: shock, pulsatile abdominal mass, abdominal pain β suggest rupture; urgent surgery.
- Imaging:
- Ultrasound: test of choice for asymptomatic AAA (94-100% sensitivity).
- CT with IV contrast: preferred for symptomatic patients (caution in renal failure).
- MRI/MRA: rarely used emergently.
- X-ray: may show calcifications.
- Labs if rupture suspected: CBC, chemistry, coagulation, ECG.
Physical Exam
- Pulsatile supraumbilical abdominal mass.
- Signs of rupture: hypotension, tachycardia, shock, flank contusion (Grey Turner sign).
- Possible vertebral erosion, ureteral obstruction, embolic ischemia to legs.
Differential Diagnosis
- Other abdominal masses, GI or renal causes of abdominal/back pain, hernias, bowel obstruction, GI hemorrhage, arthritis, metastasis, MI.
Treatment
General Measures
- Control atherosclerotic risk factors: HTN, dyslipidemia, diabetes, smoking cessation.
- Smoking doubles AAA growth rate (~0.35 mm/year).
- Emergent vascular surgery consult for unstable or symptomatic patients; IV access, resuscitation, bedside ultrasound.
- Elective repair recommended based on size and risk factors.
Medications
- Ξ²-blockers, aspirin, statins: may reduce AAA growth and complications; recommended for CAD risk reduction.
- ACE inhibitors: inconclusive on growth; may reduce rupture risk.
- Doxycycline, roxithromycin: no proven effect on AAA.
Surgery
- Elective repair threshold: diameter β₯5.5 cm in average patient.
- Consider earlier repair (4.5-5 cm) in women or high rupture risk patients.
- High risk for rupture: rapid expansion (>0.5 cm/6 months), uncontrolled HTN, smoking, severe COPD.
- Perioperative mortality ~5% for elective open repair.
- Endovascular AAA repair (EVAR) preferred for ruptured AAA in high-risk patients; similar 30-day mortality to open repair.
- Contraindications to EVAR: aortic neck >32 mm or neck length <7 mm for ruptured AAA.
Admission and Inpatient Care
- Monitor for abdominal compartment syndrome (4-12%), especially post-large fluid resuscitation.
Follow-Up
- Post-open repair CT at 5 years to assess late complications.
- Tailor imaging and surveillance postoperatively.
- Aggressive risk factor modification post-op mandatory.
Diet
- Low-fat, low-salt, low-caffeine diet.
- Optimize nutrition pre-elective repair.
Patient Education
- Smoking cessation, aerobic exercise, and aggressive control of cardiovascular risk factors.
Prognosis
- Progressive disorder; average expansion 0.3-0.4 cm/year.
- Fast expansion >0.6 cm/year needs evaluation for surgery.
- Rupture risk increases with diameter >5.5 cm, rapid growth, female sex, recent surgery, uncontrolled HTN.
Complications
- MI, respiratory failure, acute kidney injury (early).
- Graft infection, aortoenteric fistula, graft occlusion (late).
- Ischemic bowel, abdominal compartment syndrome post-rupture and open repair.
References
- Chaikof EL, Dalman RL, Eskandari MK, et al. Society for Vascular Surgery guidelines on AAA care. J Vasc Surg. 2018;67(1):2-77.e2.
- LeFevre ML; USPSTF recommendation on AAA screening. Ann Intern Med. 2014;161(4):281-290.
- Guessous I, Periard D, Lorenzetti D, et al. Pharmacotherapy for AAA expansion: systematic review. PLoS One. 2008;3(3):e1895.
- Braithwaite B, Cheshire NJ, Greenhalgh RM, et al; IMPROVE Trial. EVAR vs open repair outcomes. Eur Heart J. 2015;36(31):2061-2069.
See Also
- Aortic Dissection
- Arteritis, Temporal
- Ehlers-Danlos Syndrome
- Marfan Syndrome
- Polyarteritis Nodosa
- Turner Syndrome
ICD10 Codes
- I71.4 Abdominal aortic aneurysm, without rupture
- I71.3 Abdominal aortic aneurysm, ruptured
Clinical Pearls
- Men 65-75 with smoking history should have one-time ultrasound screening.
- Screening intervals depend on aneurysm size; larger aneurysms require more frequent imaging.
- Ruptured AAA presents with shock, abdominal pain, pulsatile mass; bedside ultrasound is vital.
- EVAR and open repair have similar mortality but EVAR has lower perioperative morbidity.
- Aggressive risk factor control, especially smoking cessation, is crucial.