Erythema Nodosum
BASICS
DESCRIPTION
- Delayed-type IV hypersensitivity panniculitis affecting subcutaneous fat.
- Presents with multiple, bilateral, erythematous, tender nodules usually on the anterior shins.
- Lesions evolve color like bruises, no ulceration (unlike erythema induratum).
- Common prodrome: fever, weight loss, arthralgia.
- Usually self-limited, remitting spontaneously within weeks to months without scarring.
- Divided into acute (common) and chronic (rare).
- Pediatric variant often limited to palms/soles, unilateral, shorter duration.
- May recur during pregnancy.
EPIDEMIOLOGY
- Most frequent in women aged 18-34 years.
- Incidence 1-5 per 100,000 per year.
- Female predominance (6:1).
- Geographic variation based on associated disorders prevalence.
ETIOLOGY AND PATHOPHYSIOLOGY
- Idiopathic: up to 55%.
- Infectious causes (44%):
- Most common: streptococcal pharyngitis
- Others: mycobacteria, mycoplasma, chlamydia, coccidioidomycosis, Campylobacter, rickettsiae, Salmonella, syphilis.
- Sarcoidosis (11-25%).
- Drugs (3-10%): sulfonamides, amoxicillin, oral contraceptives, bromides, azathioprine, vemurafenib.
- Pregnancy (2-5%).
- Enteropathies (1-4%): ulcerative colitis, Crohn disease, Behçet disease, celiac disease, diverticulitis.
- Rare causes (<1%): fungal infections, viral/chlamydial, malignancies, Sweet syndrome, COVID-19 and SARS-CoV-2 vaccine.
RISK FACTORS
- Underlying infections, systemic diseases, drug exposures as above.
DIAGNOSIS
HISTORY
- Prodrome 1-3 weeks prior: fever, malaise, weight loss, cough, arthralgia.
- Tender, erythematous nodules mainly on shins.
- May have headache, chills, fatigue.
- Systemic symptoms may precede skin lesions.
PHYSICAL EXAM
- Warm, tender, erythematous nodules and plaques on anterior shins; may extend proximally or to other sites.
- Nodules 1-10 cm, poorly demarcated.
- Color changes resemble bruises (erythema contusiformis).
DIFFERENTIAL DIAGNOSIS
- Nodular vasculitis/erythema induratum (ulcerative).
- Superficial thrombophlebitis.
- Cellulitis.
- Weber-Christian disease.
- Lupus panniculitis.
- Cutaneous polyarteritis nodosa.
- Sarcoidal granulomas.
- Cutaneous T-cell lymphoma.
- Infectious panniculitis (various organisms).
DIAGNOSTIC TESTS
- Labs: ESR/CRP often elevated, CBC mild leukocytosis.
- Throat culture, ASO titer, blood/stool cultures as indicated.
- Tuberculin skin test.
- CXR to evaluate for sarcoidosis or TB.
- Biopsy rarely necessary except atypical or chronic cases.
- Histology: septal panniculitis without vasculitis, early neutrophilic infiltrate, Miescher radial granulomas (histiocytes with stellate clefts), late fibrosis and giant cells.
- Cutaneous ultrasound may show mixed lobular/septal panniculitis.
TREATMENT
GENERAL MEASURES
- Usually self-limited within 1-2 months.
- Supportive: mild compression, leg elevation for pain relief.
- Discontinue causative drugs.
- Treat underlying disorder if identified.
MEDICATION
First Line
- NSAIDs:
- Ibuprofen 400 mg q4-6h (max 3200 mg/day)
- Indomethacin 25-50 mg TID
- Naproxen 250-500 mg BID
- Caution: GI effects, fluid retention, renal insufficiency, CV risk, interactions with diuretics and β-blockers.
Second Line
- Potassium iodide 400-900 mg/day divided for 3-4 weeks (monitor thyroid function, pregnancy class D).
- Corticosteroids for severe/refractory cases: prednisone 1 mg/kg/day for 1-2 weeks (side effects: hyperglycemia, hypertension, weight gain, mood changes, osteoporosis).
- Colchicine (Behçet disease-associated EN): 0.6-1.2 mg BID (GI upset common).
ONGOING CARE
- Elevate legs, consider elastic support stockings during ambulation.
- Monitor monthly or per underlying disease course.
PATIENT EDUCATION
- Lesions resolve in weeks to months, unlikely to scar.
- Joint symptoms may persist.
- Avoid causative drugs and exposures.
PROGNOSIS
- Lesions resolve in 2 weeks on average; total course 6-12 weeks.
- Recurrences possible, especially in sarcoidosis, streptococcal infections, pregnancy, oral contraceptive use.
COMPLICATIONS
- Dependent on underlying condition.
- EN lesions themselves typically do not cause complications.
REFERENCES
- Chowaniec M, Starba A, Wiland P. Erythema nodosum—review of the literature. Reumatologia. 2016;54(2):79-82.
- Laborada J, Cohen PR. Tuberculosis-associated erythema nodosum. Cureus. 2021;13(12):e20184.
- Schwartz RA, Nervi SJ. Erythema nodosum: a sign of systemic disease. Am Fam Physician. 2007;75(5):695-700.
- Xie Y, Yin B, Shi X. Erythema nodosum following SARS-CoV-2 vaccine. J Eur Acad Dermatol Venereol. 2022;36(10):e752-e753.
CODES
- ICD10 L52 Erythema nodosum
- ICD10 A18.4 Tuberculosis of skin and subcutaneous tissue
CLINICAL PEARLS
- EN presents as erythematous patches with palpable underlying nodularity.
- Evaluation for systemic causes essential despite high rate of idiopathic cases.
- Presence of hilar adenopathy is not specific for sarcoidosis.
- In Hodgkin lymphoma patients, EN may herald recurrence.