Esophageal Varices
BASICS
DESCRIPTION
- Dilated submucosal veins connecting portal and systemic circulation in distal esophagus.
- Result from portal hypertension, usually due to cirrhosis.
- Variceal rupture is the leading fatal complication of cirrhosis.
- Severity of liver disease correlates with varices presence and bleeding risk.
EPIDEMIOLOGY
- At diagnosis, 30% of cirrhotics have varices; 90% at 10 years.
- 1-year first bleed risk: 5% (small varices), 15% (large varices).
- 50% of variceal patients experience bleeding during their disease.
- Bleeding mortality 10-20% within 6 weeks.
- Male predominance.
ETIOLOGY AND PATHOPHYSIOLOGY
- Portal hypertension increases resistance to portal flow at hepatic sinusoids via vasoconstriction, sinusoidal remodeling.
- Increased portal flow due to splanchnic arterial vasodilation mediated by nitric oxide, prostacyclin, TNF.
- Causes:
- Prehepatic: portal vein thrombosis, splenomegaly.
- Intrahepatic: cirrhosis (most common), schistosomiasis, fatty liver, granulomatous diseases.
- Posthepatic: Budd-Chiari syndrome, right heart failure.
RISK FACTORS
- Cirrhosis severity, thrombocytopenia, splenomegaly.
- Varix size, endoscopic red signs, variceal wall thickness, portal pressure changes.
- MELD/Child-Pugh score, portal vein thrombosis, hepatic venous pressure gradient (HVPG).
DIAGNOSIS
HISTORY
- Underlying liver disease or cirrhosis.
- Risk factors: alcohol abuse, hepatitis B/C, IV drug use.
- Presentation with hematemesis, melena, hematochezia.
- Rapid bleeding may present as rectal bleeding.
PHYSICAL EXAM
- Hemodynamic instability signs: hypotension, tachycardia.
- Signs of chronic liver disease: small firm liver, splenomegaly, ascites.
- Caput medusae, spider angiomas, palmar erythema.
- Rectal varices, blood on digital rectal exam.
- Hepatic encephalopathy signs.
DIFFERENTIAL DIAGNOSIS
- Upper GI bleeding: peptic ulcer, gastritis, malignancy, Mallory-Weiss tear, arteriovenous malformations.
- Lower GI bleeding: hemorrhoids, diverticulosis, malignancy.
DIAGNOSTIC TESTS
- Labs: anemia, thrombocytopenia, liver function tests, prolonged PT, elevated BUN.
- Endoscopy (EGD): identifies varices, bleeding, red wale marks; enables band ligation.
- Transient elastography (Fibroscan): risk stratification for portal hypertension.
- HVPG measurement: gold standard for portal pressure.
- Doppler US, CT/MRI angiography (second line).
TREATMENT
GENERAL MEASURES
- Treat underlying liver disease and complications.
- Resuscitate with IV fluids and blood products (avoid overtransfusion).
- Avoid sedation and nephrotoxic drugs during bleeding.
- Use vasoactive agents (octreotide, terlipressin) to reduce portal pressure.
MEDICATION
First Line
- Nonselective Ξ²-blockers (NSBB): propranolol, nadolol, carvedilol for primary prophylaxis to reduce first bleed risk.
- NSBB dosing titrated to reduce heart rate by ~25%.
- Carvedilol may be more effective in reducing portal pressure.
Secondary Prevention
- Combination of NSBB and endoscopic variceal ligation (EVL) reduces rebleeding risk.
- Proton pump inhibitors during EVL to reduce complications.
ENDOSCOPIC THERAPY
- Variceal band ligation preferred over sclerotherapy.
- Repeated ligation for eradication and rebleeding control.
OTHER PROCEDURES
- Balloon tamponade or self-expanding metal stents for temporary bleeding control.
- Transjugular intrahepatic portosystemic shunt (TIPS) for refractory cases.
- Liver transplantation for definitive treatment.
ISSUES FOR REFERRAL
- Urgent endoscopy for diagnosis and treatment.
- Referral for TIPS or liver transplant evaluation.
- Management of portal hypertension complications.
ONGOING CARE
FOLLOW-UP
- Surveillance endoscopy every 1-4 weeks during variceal eradication.
- Routine screening endoscopy every 1-3 years in compensated cirrhosis.
- Avoid unnecessary endoscopy in low-risk patients (TE <20 kPa, platelets >150,000).
PATIENT EDUCATION
- Lifestyle modifications to reduce liver injury.
- Importance of adherence to medications and follow-up.
PROGNOSIS
- 1-year survival ~50% after variceal bleeding; mortality correlates with liver disease severity.
- Recurrence of varices and bleeding common without prophylaxis.
COMPLICATIONS
- Rebleeding, infection, hepatic encephalopathy, renal dysfunction, hepatorenal syndrome.
- Formation of gastric varices post-eradication.
REFERENCES
- Jakab SS, Garcia-Tsao G. Evaluation and management of esophageal and gastric varices in patients with cirrhosis. Clin Liver Dis. 2020;24(3):335-350.
- Simonetto DA, Liu M, Kamath PS. Portal hypertension and related complications: diagnosis and management. Mayo Clin Proc. 2019;94(4):714-726.
CODES
- ICD10 I85.0 Esophageal varices
- ICD10 I85 Esophageal varices
- ICD10 I85.1 Secondary esophageal varices
CLINICAL PEARLS
- Thrombocytopenia is a sensitive marker for portal hypertension and large varices.
- Half of cirrhotics have varices; one-third will bleed.
- Bleeding risk increases with varice size and red wale marks.
- Avoid Ξ²-blockers during active bleeding.
- Overtransfusion increases portal pressure and bleeding risk.