BASICS
Description
- Excessive coarse, pigmented terminal hair in male distribution on body and face.
- Can be ethnic or due to androgen excess.
- Commonly seen in PCOS (hirsutism, acne, menstrual irregularities, obesity).
Epidemiology
- Prevalence: 5-10% of reproductive-age women.
Etiology and Pathophysiology
- Increased androgenic hormones from ovaries, adrenals, or peripheral conversion.
- Idiopathic (increased peripheral androgen binding).
- Can be secondary to androgen-secreting tumors or medication use.
- Multifactorial genetics.
Risk Factors
- Family history, ethnicity (Ashkenazi Jews, Mediterranean).
- Obesity.
General Prevention
- Counseling for late-onset CAH carriers.
Commonly Associated Conditions
- PCOS (most common cause)
- Acne
- Central obesity
- Virilization (rapid onset, clitoromegaly, balding, deep voice).
DIAGNOSIS
History
- Onset, severity, progression.
- Weight, BMI.
- Psychosocial impact.
- Menstrual and fertility history.
- Severe acne, virilization.
- Medication review (valproic acid, testosterone, danazol, glucocorticoids).
- Galactorrhea presence.
Physical Exam
- Hair growth in chin, neck, sideburns, lower back, sternum, areola, abdomen, shoulders, buttocks, perineum, inner thighs.
- Acne, striae, acanthosis nigricans.
- Virilization signs.
- Ferriman-Gallwey scale (0–4 in 9 areas; >8 positive; 8-15 mild, 16-25 moderate, >25 severe).
Differential Diagnosis
- PCOS (72-82%)
- Idiopathic hyperandrogenemia (6-15%)
- Idiopathic hirsutism (4-7%)
- Late-onset/non-classic CAH (2-4%)
- Androgen-secreting tumors (0.2%)
- Thyroid dysfunction, hyperprolactinemia
- Cushing syndrome, acromegaly
- Medication side effects.
Diagnostic Tests
- Early morning 17-hydroxyprogesterone for NCCAH screening.
- PCOS diagnosis: 2/3 criteria—menstrual dysfunction, hyperandrogenemia, polycystic ovaries.
- Random total testosterone; repeat with free testosterone if normal but clinical suspicion remains.
- Testosterone >150-200 ng/dL → imaging for ovarian/adrenal tumors.
- Metabolic screening (fasting glucose, lipids, waist circumference, BP).
- Prolactin, FSH, LH, TSH if amenorrheic.
- DHEA-S if virilization.
TREATMENT
General Measures
- Tailored to patient preference and psychosocial impact.
- Decrease new hair growth and improve metabolic profile.
- Weight loss for overweight/obese.
- Treat associated acne.
- Provide contraception as needed.
Medications
First Line
- Oral contraceptives to suppress ovarian androgen production and increase SHBG; improve menstrual irregularities.
- Use progestins with antiandrogenic properties (norgestimate, desogestrel, drospirenone).
- Eflornithine cream (Vaniqa): topical, slows facial hair growth (indefinite use).
- Combination of OCPs and antiandrogens reserved for severe cases or after 6 months OCP failure.
Second Line
- Antiandrogens (with OCPs):
- Spironolactone 50-200 mg/day (monitor potassium; avoid in pregnancy).
- Finasteride 2.5-7.5 mg/day (off-label; pregnancy Category X).
- Cyproterone (not available in US).
- Leuprolide 3.75 mg IM monthly (side effects: bone loss, dryness, avoid in pregnancy).
- Flutamide not recommended (hepatotoxicity).
- Cosmetic hair removal: temporary (shaving, waxing) or permanent (laser preferred; electrolysis for light hair).
Pregnancy Considerations
- Related infertility possible.
- Hormonal treatments contraindicated.
- Provide contraception as needed.
Complementary Medicine
- Glycyrrhiza uralensis and Paeonia lactiflora may lower androgen levels (limited evidence).
ONGOING CARE
- Monitor medication side effects.
- Encourage low-calorie, low-glycemic diet in PCOS patients.
PATIENT EDUCATION
- Hormonal treatments prevent new hair growth but do not reverse existing hair.
- Cosmetic removal may be needed for present hair.
- Treatment takes at least 6 months.
PROGNOSIS
- Good for halting new hair growth.
- Moderate to poor for reversing existing hair.
COMPLICATIONS
- PCOS-related: dysfunctional uterine bleeding → anemia, endometrial hyperplasia, cancer risk.
- Androgen excess may worsen lipid profile, cardiac risk, and bone density.
REFERENCES
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Martin KA, Anderson RR, Chang RJ, et al. Evaluation and treatment of hirsutism in premenopausal women: an endocrine society clinical practice guideline. J Clin Endocrinol Metab. 2018;103(4):1233-1257.
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Matheson E, Bain J. Hirsutism in women. Am Fam Physician. 2019;100(3):168-175.
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Goodman NF, Cobin RH, Futterweit W, et al; American Association of Clinical Endocrinologists, American College of Endocrinology, Androgen Excess and PCOS Society. Guide to the best practices in evaluation and treatment of PCOS—part 1. Endocr Pract. 2015;21(11):1291-1300.
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American College of Obstetricians and Gynecologists' Committee on Practice Bulletins—Gynecology. ACOG practice bulletin no. 194: polycystic ovary syndrome. Obstet Gynecol. 2018;131(6):e157-e171.
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Williams T, Moore JB, Regehr J. Polycystic ovary syndrome: common questions and answers. Am Fam Physician. 2023;107(3):264-272.
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Arentz S, Abbott JA, Smith CA, et al. Herbal medicine for PCOS and hyperandrogenism: review of lab evidence with clinical findings. BMC Complement Altern Med. 2014;14:511.