BASICS
Description
- Hyperthyroidism: Excess thyroid hormone production from the thyroid gland.
- Thyrotoxicosis: Clinical syndrome of thyroid hormone excess; may be from thyroid or other sources.
- Causes include Graves disease (GD), toxic multinodular goiter (TMNG), toxic adenoma, thyroiditis, iodine-induced, drug-induced, and subclinical forms.
- Thyroid storm: Severe thyrotoxicosis with fever, tachycardia, GI symptoms, CNS dysfunction; ~50% mortality.
Geriatric Considerations
- Symptoms may be atypical or absent.
- Atrial fibrillation common when TSH <0.1 mIU/L.
Pediatric Considerations
- Treated with antithyroid drugs for 12-24 months.
- Radioactive iodine therapy controversial.
Pregnancy Considerations
- PTU preferred in 1st trimester; methimazole in 2nd/3rd trimesters.
- Use lowest effective dose; avoid treatment-induced hypothyroidism.
- Radioiodine contraindicated.
EPIDEMIOLOGY
- Prevalence: 1.3% of population.
- Female > male (7β10:1 ratio).
- GD common in 2nd-3rd decades; TMNG in >40 years.
ETIOLOGY AND PATHOPHYSIOLOGY
- Graves disease: Autoimmune with TSH receptor antibodies.
- TMNG: TSH receptor gene abnormalities (60%).
- Toxic adenoma: TSH receptor mutation.
- Hashitoxicosis: Autoimmune thyroiditis with antimicrosomal antibodies.
- Subacute thyroiditis: Viral granulomatous inflammation.
- Drug-induced: Amiodarone, lithium, interferon-Ξ±, interleukin-2.
- Postpartum thyroiditis: Autoimmune; hypothyroidism in 60%.
Genetics
- GD concordance ~35% in monozygotic twins.
RISK FACTORS
- Positive maternal family history.
- Other autoimmune diseases.
- Iodide repletion after deprivation.
COMMONLY ASSOCIATED CONDITIONS
- Autoimmune disorders.
- Down syndrome.
DIAGNOSIS
History
- Hypermetabolic symptoms: fatigue, weakness, weight loss, heat intolerance.
- Neuropsychiatric: agitation, anxiety, psychosis, poor concentration.
- GI: increased appetite, hyperdefecation.
- Gynecologic: oligomenorrhea, amenorrhea.
- Cardiovascular: tachycardia, chest discomfort.
- Geriatric: apathetic hyperthyroidism.
Physical Exam
- Skin: warm, moist; pretibial myxedema (GD).
- Eyes: exophthalmos, lid lag.
- Endocrine: goiter, gynecomastia, hyperhidrosis.
- Cardiovascular: tachycardia, atrial fibrillation.
- Neurologic: tremor, proximal muscle weakness.
Differential Diagnosis
- Anxiety, depression.
- Diabetes mellitus.
- Pregnancy, menopause.
- Pheochromocytoma, carcinoid syndrome.
Diagnostic Tests
- Suppressed TSH, elevated free T4 (95% cases).
- T3 elevated in T3 toxicosis or amiodarone-induced thyrotoxicosis.
- TSH receptor antibodies diagnostic for GD.
- Nuclear medicine uptake: GD shows diffuse uptake; TMNG heterogeneous; toxic nodule focal "hot" nodule.
- Neck ultrasound: increased vascularity in GD.
TREATMENT
Observation
- Mild hyperthyroidism may be observed, especially in young low-risk patients.
Medications
- Antithyroid drugs: Methimazole preferred, PTU in thyroid storm and 1st trimester pregnancy.
- Duration: 12-18 months; relapse common after cessation.
- Side effects: hepatitis, agranulocytosis.
- Beta blockers: Symptom control; propranolol inhibits T4 to T3 conversion.
- Glucocorticoids: Reduce T4 to T3 conversion; used in thyroid storm and Graves ophthalmopathy.
- Cholestyramine: Reduces thyroid hormone reabsorption.
- Other: Lithium, iodine solutions (SSKI), with careful timing to avoid Jod-Basedow.
Radioactive iodine therapy (RAIT)
- Used in GD, TMNG.
- Pretreat with antithyroid drugs.
- Hypothyroidism common post-RAIT.
Surgery
- Indicated for compressive symptoms, malignancy, or contraindications to other therapies.
- Preferred in 2nd trimester pregnancy.
ISSUES FOR REFERRAL
- Graves ophthalmopathy to ophthalmology.
ONGOING CARE
Monitoring
- Thyroid function tests q3 months.
- CBC and LFTs during antithyroid therapy.
- Post-RAIT: thyroid tests at 6, 12, 24 weeks, then annually.
- Smoking cessation in GD.
Diet
- Maintain sufficient calories.
PROGNOSIS
- Good with early diagnosis and treatment.
- High relapse rates with antithyroid drugs alone in GD.
COMPLICATIONS
- Surgery: hypoparathyroidism, recurrent laryngeal nerve injury, hypothyroidism.
- RAIT: postablation hypothyroidism.
- GD: relapse, ophthalmopathy, atrial fibrillation, heart failure, CVA.
REFERENCES
- Cappola AR, Fried LP, Arnold AM, et al. Thyroid status, cardiovascular risk, and mortality in older adults. JAMA. 2006;295(9):1033-1041.
- Bahn RS, Burch HB, Cooper DS, et al. Hyperthyroidism and other causes of thyrotoxicosis: management guidelines of the American Thyroid Association and American Association of Clinical Endocrinologists. Endocr Pract. 2011;17(3):456-520.
- Bahn Chair RS, Burch HB, Cooper DS, et al. Hyperthyroidism and other causes of thyrotoxicosis: management guidelines of the American Thyroid Association and American Association of Clinical Endocrinologists. Thyroid. 2011;21(6):593-646.
Clinical Pearls
- Not all thyrotoxicoses are due to hyperthyroidism.
- Graves disease typically presents with hyperthyroidism, ophthalmopathy, and goiter.
- Thyroid storm is a medical emergency.
- TSH levels may lag in normalization after treatment despite decreasing T3/T4.