Pituitary Adenoma
BASICS
- Definition: Benign, slow-growing tumor of the pituitary gland; may secrete hormones or cause mass effects.
- Subtypes (hormonal):
- Prolactinoma (PRL): 25–40%
- Nonfunctioning: 30%
- Somatotroph (GH): 15–20%
- Corticotroph (ACTH): 5–10%
- Thyrotroph (TSH): <1%
- Gonadotroph (LH/FSH), Mixed
- Microadenoma: <10 mm; Macroadenoma: ≥10 mm
EPIDEMIOLOGY
- Prevalence (autopsy): Microadenomas 3–27%, Macroadenomas <0.5%
- Clinically apparent: 18/100,000 people
ETIOLOGY & PATHOPHYSIOLOGY
- Origin: Monoclonal adenohypophysial cell growth
- Diagnosis often prompted by:
- Hormonal effects (functional microadenoma)
- Mass effect (visual field deficits, headache)
- Genetic associations:
- 15% have AIP gene mutation (familial isolated pituitary adenoma); tend to be younger and larger tumors
RISK FACTORS
- Multiple endocrine neoplasia (MEN1)
- McCune-Albright syndrome
DIAGNOSIS
History
- Hyperprolactinemia: infertility, amenorrhea, galactorrhea, gynecomastia, impotence
- Mass effect: headache, bitemporal hemianopsia (visual field loss)
- Acromegaly (GH excess): coarse features, hand/foot swelling, carpal tunnel, LVH
- Cushing disease (ACTH excess): moon face, truncal obesity, striae, hirsutism
- Apoplexy: sudden headache/collapse (rare, life-threatening)
- Secondary hormone deficiencies: FTT in children, hypogonadism, secondary hypothyroidism or adrenal insufficiency
Physical Exam
- Visual deficits: bitemporal hemianopsia
- Acromegaly: coarse features, diaphoresis
- Cushingoid features: central obesity, fat pad, striae, hirsutism
- Hypopituitarism: failure to thrive, hypotension, hypoglycemia
Differential Diagnosis
- Pituitary hyperplasia (e.g., pregnancy, hypothyroidism), Rathke cleft cyst, craniopharyngioma, metastatic tumor, lymphocytic hypophysitis, granulomatous disease
Diagnostic Testing
- Hormonal Panel:
- PRL, GH, IGF-1, ACTH, 24-hr urinary-free cortisol, overnight DMST, β-HCG, FSH, LH, TSH, free T4
- Imaging: MRI is gold standard (>90% sensitivity/specificity)
- Specialized testing: Octreotide scan (somatostatin receptor), oral glucose suppression test for acromegaly, macimorelin test for adult GH deficiency
Lab Patterns by Subtype
- Prolactinoma: PRL >20 ng/mL
- Acromegaly: ↑IGF-1, failure of GH suppression on glucose test
- Cushing disease: ↑24h urinary cortisol, abnormal DMST, ACTH level
- TSH-oma: Both TSH & free T4 ↑ (central hyperthyroidism)
- Nonfunctioning: usually mass effect
TREATMENT
Medical Therapy (First Line)
- Prolactinoma: Dopamine agonists
- Cabergoline: 0.25 mg 1–2x/week, titrate per PRL
- Bromocriptine: 1.25–2.5 mg PO daily, titrate as needed
- Somatotroph (GH): Somatostatin analogs (octreotide, lanreotide), pegvisomant (GH receptor antagonist)
- Corticotroph (ACTH): Mitotane, ketoconazole, pasireotide, mifepristone
- Second line: Metyrapone, octreotide (gonadotropinoma, thyrotropinoma)
Surgical Therapy
- Indications: Symptomatic macroadenomas (mass effect, vision loss), non-PRL tumors
- Approach: Endoscopic transsphenoidal resection is preferred
Adjunct Therapy
- Radiotherapy: Fractionated or stereotactic (for residual or recurrent tumor)
- Medical adjunct: Used if surgery incomplete/contraindicated or as adjuvant to reduce recurrence
Referral
- Neurosurgery for symptomatic macroadenoma (except PRL, usually medical first)
- Endocrinology for hormonal evaluation and long-term follow-up
ONGOING CARE
- Imaging: MRI at 6 and 12 months post-surgery, then per clinical judgment
- Hormonal labs: Monitor involved hormone(s) post-op; hypopituitarism may develop 10–15 years after radiotherapy
PROGNOSIS
- Depends on: Subtype, size, response to therapy, surgical success
- Complications:
- Post-op: transient diabetes insipidus, hypogonadism
- Apoplexy (acute hemorrhagic infarction): surgical emergency
- Nelson syndrome (post-adrenalectomy rapid tumor growth)
- Chronic: pituitary hormone insufficiency, optic neuropathy (after >60 Gy radiation)
ICD-10
- D35.2 Benign neoplasm of pituitary gland
CLINICAL PEARLS
- Incidentaloma: Asymptomatic microadenoma on imaging; screen for PRL, GH/IGF-1, ACTH/cortisol, FSH, LH, TSH, free T4
- Initial therapy: Dopamine agonist for PRLs, surgery for others
- Pituitary apoplexy: Sudden hemorrhagic infarction—fatal without decompression