Seizure Disorder, Focal
BASICS
- Definition: Seizures from abnormal synchronous neuronal discharges limited to one hemisphere (“focal” or “partial”).
- Classification:
- Focal aware (simple partial): No impairment of awareness
- Focal impaired awareness (complex partial): Impaired responsiveness/awareness
- Motor onset: Tonic, clonic, myoclonic, or other motor symptoms
- Nonmotor onset: Sensory, autonomic, cognitive, or emotional features
EPIDEMIOLOGY
- Prevalence: ~20 per 100,000 persons in the US
- Etiology by age:
- Early childhood: developmental malformation, trauma
- Young adults: developmental, infection, trauma
- Middle/older adults: stroke, trauma, infection, neoplasm
ETIOLOGY & PATHOPHYSIOLOGY
- Focal onset: Abnormal depolarization of neuronal network in one hemisphere; can stay local or spread.
- Symptoms: Depend on location (motor, sensory, temporal, parietal, occipital)
- Genetics: E.g., benign rolandic epilepsy (autosomal dominant)
- Other risk factors: TBI, thiamine deficiency
RISK FACTORS
- History of TBI
- Thiamine-deficient formula in infancy
- Drugs/lower seizure threshold (tramadol, bupropion, cocaine, theophylline)
- Prior neurologic disease
COMMONLY ASSOCIATED CONDITIONS
- Depression
DIAGNOSIS
HISTORY
- Detailed eyewitness account is crucial
- Duration: seconds–minutes unless status epilepticus
- Review meds and substance use
- Ask about prior TBI, comorbidities
FEATURES
Focal aware (simple partial): - Motor onset: tonic/clonic movements, can show Jacksonian march - Nonmotor onset: sensory symptoms, visual/auditory/olfactory hallucinations, déjà vu, autonomic changes - Todd paralysis: temporary weakness post-seizure
Focal impaired awareness (complex partial): - May start with aura (sensory, psychic, autonomic) - Amnesia for the event, postictal confusion - Automatisms: lip smacking, picking, wandering - Commonly temporal or frontal origin
PHYSICAL EXAM
- Neurologic exam, look for lateralizing signs
DIFFERENTIAL DIAGNOSIS
- Syncope
- Psychogenic nonepileptic seizure
- Hypoglycemia
- TIA, hemiplegic migraine
- Other paroxysmal events
DIAGNOSTIC TESTS
- Lab: CBC, metabolic panel, urinalysis, drug screen, AED levels if relevant
- Serum prolactin/CK: May be elevated postictally (within 10–20 min for prolactin, 6–24h for CK); may help distinguish true seizure from psychogenic
- EEG: Consider for all first unprovoked seizures (best yield within 24h, especially with sleep deprivation)
- Imaging: CT/MRI to rule out acute/structural causes (esp. new seizure, older age, abnormal exam)
- CSF: If infection suspected
- Video-EEG: For diagnostic uncertainty
TREATMENT
GENERAL MEASURES
- Maintain seizure diary (identify triggers: sleep deprivation, stress, drugs, menses, alcohol withdrawal)
- Driving: Most states restrict driving after seizures; counsel accordingly
MEDICATION
- After a single unprovoked seizure: Shared decision-making; AEDs decrease recurrence risk over 2 years but do not affect long-term remission/mortality; increased risk of side effects with immediate AED use
- First-line AEDs for focal epilepsy:
- Carbamazepine: Sodium channel blocker; SE: GI distress, hyponatremia, diplopia, rare marrow suppression/rash (screen Asians for HLA-B*1502)
- Oxcarbazepine: Similar to carbamazepine; less marrow suppression; SE: dizziness, diplopia, hyponatremia
- Lamotrigine: Sodium channel blocker; SE: insomnia, ataxia, serious rash risk (esp. with valproate; titrate slowly)
- Levetiracetam: Multiple mechanisms; SE: sedation, irritability, ataxia
- Second-line/adjuncts: Phenytoin, phenobarbital, valproate, topiramate, gabapentin, pregabalin, zonisamide
- AEDs & pregnancy: All women of childbearing age on AEDs need folate. Avoid valproate and phenytoin if possible (risk of fetal malformation)
- Monitor: AED levels as appropriate, especially in pregnancy, if toxicity suspected, or for breakthrough seizures
REFERRAL/ADDITIONAL THERAPIES
- Refer to epilepsy specialist for refractory seizures
- Vagal nerve stimulator or deep brain stimulation for refractory cases
- Surgery: Resection for refractory focal epilepsy with localized focus (pre-op Wada test, MRI, etc.)
- Ketogenic/low-glycemic diet: Can help in some refractory cases
ONGOING CARE
- Avoid triggers: Alcohol, sleep deprivation, drug use
- Driving/safety counseling
- Monitor AED side effects and drug interactions
- Follow-up: Regular review of seizure diary, labs, and imaging as needed
PROGNOSIS
- ~30% risk of recurrence after a first seizure
- Most recurrences occur within 6 months–2 years
- About 25–30% of focal epilepsies are refractory to current AEDs
- Benign rolandic epilepsy: good prognosis; temporal lobe epilepsy: often persistent
COMPLICATIONS
- Injury (accidental, e.g., falls, burns)
- Depression, anxiety, memory/cognitive impairment
ICD-10
- G40.109: Local-rel symptomatic epilepsy with simple partial seizures, not intractable, w/o status
- G40.209: Local-rel symptomatic epilepsy with complex partial seizures, not intractable, w/o status
- G40.119: Local-rel symptomatic epilepsy with simple partial seizures, intractable, w/o status
CLINICAL PEARLS
- Focal seizures arise from a discrete focus, classified by awareness and motor/nonmotor onset
- EEG and neuroimaging (CT/MRI) should be considered in first-time seizures
- Postictal prolactin and CPK help distinguish physiologic from psychogenic seizures
- Treatment after a first seizure is controversial; consider AED if structural cause or high risk of injury
- 50% respond to first AED; many require combination therapy or advanced therapies if refractory